{"id":29207,"date":"2021-02-16T18:42:36","date_gmt":"2021-02-16T18:42:36","guid":{"rendered":"https:\/\/wbowe.com\/2021\/02\/16\/sattaquer-aux-cousins-de-canavan-qui-nappartiennent-pas-a-canavan\/"},"modified":"2026-09-11T22:22:34","modified_gmt":"2026-09-11T22:22:34","slug":"sattaquer-aux-cousins-de-canavan-qui-nappartiennent-pas-a-canavan","status":"publish","type":"post","link":"https:\/\/wbowe.com\/fr\/2021\/02\/16\/sattaquer-aux-cousins-de-canavan-qui-nappartiennent-pas-a-canavan\/","title":{"rendered":"37. Comprendre les cousins atteints de la maladie de Canavan non-Canavan"},"content":{"rendered":"<div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-padding-right:8%;--awb-padding-left:8%;--awb-bg-size:cover;--awb-margin-top:0px;--awb-margin-bottom:0px;\"><div class=\"fusion-column-wrapper fusion-flex-column-wrapper-legacy\"><div class=\"fusion-video fusion-vimeo fusion-aligncenter\" style=\"--awb-max-width:600px;--awb-max-height:350px;--awb-width:100%;\"><div class=\"video-shortcode\"><div class=\"fluid-width-video-wrapper\" style=\"padding-top:58.33%;\" ><iframe title=\"Vimeo video player 1\" src=\"https:\/\/player.vimeo.com\/video\/512302397?autoplay=0&amp;autopause=0\" width=\"600\" height=\"350\" allowfullscreen allow=\"autoplay; fullscreen\"><\/iframe><\/div><\/div><\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"margin-left: auto;margin-right: auto;margin-top:40px;margin-bottom:40px;width:100%;\"><div class=\"fusion-separator-border sep-double sep-dotted\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:#005b8c;border-color:#005b8c;border-top-width:1px;border-bottom-width:1px;\"><\/div><\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-text fusion-title-size-two\" style=\"--awb-margin-bottom:15px;--awb-margin-top-small:10px;--awb-margin-right-small:0px;--awb-margin-bottom-small:10px;--awb-margin-left-small:0px;\"><h2 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:34;line-height:1.36;\">S&rsquo;attaquer aux cousins de Canavan qui n&rsquo;appartiennent pas \u00e0 Canavan<\/h2><\/div><div class=\"fusion-text fusion-text-1 wjb-editors-note\"><p><strong>Note de la r\u00e9daction :<\/strong> J\u2019ai demand\u00e9 \u00e0 Joe si les branches biologiques et non biologiques figuraient toutes deux dans sa base de donn\u00e9es principale, qui compte plus de 12 000 personnes, ou bien dans une annexe. Joe explique qu\u2019il a cr\u00e9\u00e9 un arbre g\u00e9n\u00e9alogique distinct pour la branche biologique r\u00e9cemment d\u00e9couverte, et que les quantit\u00e9s d\u2019ADN partag\u00e9 correspondaient parfaitement aux g\u00e9n\u00e9rations remontant jusqu\u2019aux anc\u00eatres communs. Il raconte ensuite avoir aid\u00e9 au moins trois personnes adopt\u00e9es \u00e0 retrouver leur famille biologique \u2014 dont deux membres de la famille Canavan et une personne li\u00e9e \u00e0 Jimmy Harte \u2014 gr\u00e2ce \u00e0 l\u2019outil \u00ab correspondances partag\u00e9es \u00bb d\u2019Ancestry. Un homme, \u00ab James \u00bb, s\u2019est av\u00e9r\u00e9 \u00eatre un cousin proche des Canavan, avec une page enti\u00e8re de correspondances partag\u00e9es avec les Canavan, bien qu\u2019il pr\u00e9f\u00e8re pr\u00e9server sa vie priv\u00e9e pour l\u2019instant.<\/p>\n<\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"margin-left: auto;margin-right: auto;margin-top:40px;margin-bottom:40px;width:100%;\"><div class=\"fusion-separator-border sep-double sep-dotted\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:#005b8c;border-color:#005b8c;border-top-width:1px;border-bottom-width:1px;\"><\/div><\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-title title fusion-title-2 fusion-sep-none fusion-title-text fusion-title-size-three\" style=\"--awb-margin-top-small:10px;--awb-margin-right-small:0px;--awb-margin-bottom-small:10px;--awb-margin-left-small:0px;\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:30;line-height:1.5;\">Transcription<\/h3><\/div><div class=\"fusion-text fusion-text-2 wjb-transcript\"><p style=\"font-size: .85em; font-style: italic;\">Intervenants : <strong>WJB<\/strong> \u2014 William J. Bowe ; <strong>JH<\/strong> \u2014 Joseph Hart. Transcription \u00e0 partir de l&rsquo;enregistrement ; ponctuation ajout\u00e9e et erreurs d&rsquo;\u00e9coute manifestes corrig\u00e9es. <\/p>\n<p><strong>WJB :<\/strong> Donc, dans votre base de donn\u00e9es, vous m\u2019aviez indiqu\u00e9 que vous aviez plus de 12 000 personnes qui se situent plus ou moins l\u00e0 o\u00f9 elles devraient \u00eatre selon un certain sch\u00e9ma. Ces deux aspects, biologique et non biologique, font-ils partie de votre sch\u00e9ma global, ou votre tableau comporte-t-il une annexe ? <\/p>\n<p><strong>JH :<\/strong> Eh bien, il y a une annexe. Et je ne sais pas encore tr\u00e8s bien comment je vais r\u00e9soudre ce probl\u00e8me. Disons simplement qu\u2019une fois que j\u2019ai commenc\u00e9 \u00e0 admettre qu\u2019il s\u2019agissait d\u2019une branche \u00e0 laquelle je devais pr\u00eater attention, j\u2019ai commenc\u00e9 \u00e0 construire un arbre g\u00e9n\u00e9alogique distinct consacr\u00e9 uniquement \u00e0 cette branche, car \u00e0 ce moment-l\u00e0, c\u2019\u00e9tait encore \u00e0 des fins de recherche. J\u2019ai donc commenc\u00e9 \u00e0 constituer cet arbre g\u00e9n\u00e9alogique dans un fichier distinct \u2014 je ne l\u2019ai pas reli\u00e9 \u00e0 mon arbre g\u00e9n\u00e9alogique principal. Et toutes les personnes que j\u2019ai ajout\u00e9es, dont certaines avaient elles-m\u00eames \u00e9tabli des arbres g\u00e9n\u00e9alogiques, m\u2019ont permis de me dire : \u00ab Bon, quand j\u2019en arrive \u00e0 cet ensemble d\u2019arri\u00e8re-grands-parents, cela figure dans cet arbre g\u00e9n\u00e9alogique biologique. \u00bb Et ainsi, si leur arbre g\u00e9n\u00e9alogique correspondait d\u2019une mani\u00e8re ou d\u2019une autre \u00e0 ces grands-parents, je me disais alors : \u00ab D\u2019accord, il y a de fortes chances que je sois un cousin au deuxi\u00e8me degr\u00e9 (une fois \u00e9loign\u00e9) de cette personne. \u00bb J\u2019ai donc commenc\u00e9 \u00e0 construire cet arbre g\u00e9n\u00e9alogique, et chaque fois que j\u2019ajoutais quelqu\u2019un, si cette personne disposait d\u2019un arbre g\u00e9n\u00e9alogique li\u00e9 \u00e0 son compte ADN et que je pouvais l\u2019int\u00e9grer en tant que cousin connu, les quantit\u00e9s d\u2019ADN que j\u2019observais dans ces correspondances correspondaient globalement aux diff\u00e9rentes g\u00e9n\u00e9rations qui s\u00e9paraient leur anc\u00eatre commun de mes anc\u00eatres communs. Quoi qu\u2019il en soit, c\u2019\u00e9tait assez int\u00e9ressant d\u2019obtenir cette confirmation que, oui, toutes ces personnes que j\u2019int\u00e9grais dans ce petit arbre g\u00e9n\u00e9alogique semblaient correspondre aux bonnes g\u00e9n\u00e9rations. Et puis, permettez-moi de pr\u00e9ciser que non seulement la d\u00e9couverte de mon propre cas de non-paternit\u00e9 a \u00e9t\u00e9 l\u2019une des choses int\u00e9ressantes que j\u2019ai constat\u00e9es gr\u00e2ce \u00e0 l\u2019ADN autosomique, mais j\u2019ai \u00e9galement mis en relation au moins trois personnes adopt\u00e9es qui cherchaient \u00e0 retrouver leur famille biologique \u2014 deux d\u2019entre elles ont rejoint la branche des Canavan, et l\u2019une d\u2019elles a en fait rejoint la famille de Jimmy Harte.        <\/p>\n<p><strong>WJB :<\/strong> Waouh.<\/p>\n<p><strong>JH :<\/strong> Il y a donc eu au moins trois cas o\u00f9 une personne avait \u00e9t\u00e9 adopt\u00e9e, avait pass\u00e9 le test et avait eu l\u2019immense chance de trouver suffisamment de preuves pour que je me dise : \u00ab Oh, cette personne a un lien avec les Canavan \u00bb, ou un lien avec Jimmy Harte, ou quoi que ce soit d\u2019autre, simplement gr\u00e2ce aux correspondances ADN. Permettez-moi donc de revenir un peu en arri\u00e8re : lorsque j\u2019examine une correspondance ADN, l\u2019une des choses que vous pouvez faire est de d\u00e9couvrir quelles correspondances vous avez en commun. Ainsi, si je souhaite voir quels correspondances ADN j\u2019ai en commun avec, disons, Dennis Cassidy, je peux cliquer sur un bouton \u00e0 l\u2019\u00e9cran qui affichera les correspondances ADN que nous avons tous les deux en commun.  <\/p>\n<p><strong>WJB :<\/strong> Waouh.<\/p>\n<p><strong>JH :<\/strong> Et donc, dans l&rsquo;un de ces\u2026 \u2014<\/p>\n<p><strong>WJB :<\/strong> C&rsquo;est assez fort. C&rsquo;est tr\u00e8s fort, n&rsquo;est-ce pas ? <\/p>\n<p><strong>JH :<\/strong> Eh bien, surtout si la base de donn\u00e9es est tr\u00e8s volumineuse, comme c&rsquo;est le cas chez Ancestry. Et donc, l&rsquo;une de ces personnes appara\u00eet, James \u2014 je vais l&rsquo;appeler James, car c&rsquo;est bien James. Je ne vais pas mentionner son nom de famille, car il souhaite pr\u00e9server une certaine vie priv\u00e9e maintenant qu\u2019il sait qu\u2019il est un Canavan et non pas autre chose. Il n\u2019est pas pr\u00eat \u00e0 bouleverser la vie des gens. Je suppose qu\u2019il est simplement un peu r\u00e9ticent pour l\u2019instant \u00e0\u2026    <\/p>\n<p><strong>WJB :<\/strong> Oui.<\/p>\n<p><strong>JH :<\/strong> \u2014 il souhaite commencer \u00e0 prendre contact avec tous ses cousins biologiques. Bref. Et vous pouvez le comprendre.  <\/p>\n<p><strong>WJB :<\/strong> Oui, tout \u00e0 fait. C&rsquo;est possible. Bien s\u00fbr.  <\/p>\n<p><strong>JH :<\/strong> Parce que c&rsquo;est sans doute tr\u00e8s excitant pour lui, mais il ne veut pas perturber la vie des gens. Il s\u2019appelle donc James. Lorsque j\u2019ai examin\u00e9 les correspondances ADN que lui et moi partagions, il s\u2019agissait exclusivement de cousins Canavan. Toute cette page de correspondances communes \u00e9tait constitu\u00e9e de cousins Canavan. Je n\u2019avais donc aucun doute sur le fait qu\u2019il \u00e9tait li\u00e9 d\u2019une mani\u00e8re ou d\u2019une autre \u00e0 la famille Canavan.    <\/p>\n<p><strong>WJB :<\/strong> Oui.<\/p>\n<p><strong>JH :<\/strong> Et la quantit\u00e9 d&rsquo;ADN que nous partagions \u00e9tait si importante que nous devions \u00eatre, disons, des cousins au deuxi\u00e8me degr\u00e9, ce qui signifierait que nous aurions des arri\u00e8re-grands-parents en commun.<\/p>\n<p><strong>WJB :<\/strong> Waouh. Int\u00e9ressant. <\/p>\n<p><strong>JH :<\/strong> Et je me suis dit : \u00ab Oh mon Dieu. \u00bb \u00c7a n\u2019arrive pas tr\u00e8s souvent, mais \u00e7a s\u2019est d\u00e9j\u00e0 produit. Les deux autres fois, ce n\u2019\u00e9tait pas aussi spectaculaire. Ce n\u2019\u00e9tait pas cette page enti\u00e8re de \u2014   <\/p>\n<p><strong>WJB :<\/strong> Oui.<\/p>\n<p><strong>JH :<\/strong> \u2014 Les cousins Canavan. Bref.<\/p>\n<\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"margin-left: auto;margin-right: auto;margin-top:40px;margin-bottom:40px;width:100%;\"><div class=\"fusion-separator-border sep-double sep-dotted\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:#005b8c;border-color:#005b8c;border-top-width:1px;border-bottom-width:1px;\"><\/div><\/div><div class=\"fusion-sep-clear\"><\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div>\n","protected":false},"excerpt":{"rendered":"<p>Joe Hart explique comment il a fait face au changement qu&rsquo;un \u00e9v\u00e9nement non paternel a apport\u00e9 \u00e0 sa vision des relations familiales, m\u00eame \u00e0 trois g\u00e9n\u00e9rations de distance.<\/p>\n","protected":false},"author":2,"featured_media":20581,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"video","meta":{"_acf_changed":false,"_relevanssi_hide_post":"","_relevanssi_hide_content":"","_relevanssi_pin_for_all":"","_relevanssi_pin_keywords":"","_relevanssi_unpin_keywords":"","_relevanssi_related_keywords":"","_relevanssi_related_include_ids":"","_relevanssi_related_exclude_ids":"","_relevanssi_related_no_append":"","_relevanssi_related_not_related":"","_relevanssi_related_posts":"","_relevanssi_noindex_reason":"","footnotes":""},"categories":[1206,1036,710,709,715],"tags":[1075],"class_list":["post-29207","post","type-post","status-publish","format-video","has-post-thumbnail","hentry","category-bill-bowe-sentretient-avec-la-famille","category-c-test-adn","category-hart-fr","category-joseph-christopher-hart-fr","category-videos-de-hart","tag-family-vol-2-fr","post_format-post-format-video"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.6 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>37. Comprendre les cousins atteints de la maladie de Canavan non-Canavan - William J. Bowe<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/wbowe.com\/fr\/2021\/02\/16\/sattaquer-aux-cousins-de-canavan-qui-nappartiennent-pas-a-canavan\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"37. Comprendre les cousins atteints de la maladie de Canavan non-Canavan - William J. 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